Perioperative considerations of Noonan symdrome in adult.
DOI:
https://doi.org/10.30445/rear.v14i2.1014Keywords:
noonan syndrome, difficult airway, hemostasis alterationsAbstract
Noonan syndrome (SN) is a monogenic disease with an autosomal dominant inheritance pattern with an incidence of 1: 1500-2500. This syndrome is of particular interest to the anesthesiologist because it is considered a probable difficult airway, presenting short stature, facial dysmorphia, haemostasis, musculoskeletal and cardiological alterations, among others, whose evolution determines life expectancy reaching more advanced ages at present thanks to the control of them. Consequently, they require interventions in adulthood where there are not as many cases as in childhood. We report a case of a 53-year-old patient with NS scheduled for cervical neuroma resection with increased bleeding during surgery. Our goal is to establish a specific anesthetic plan after exposing the characteristics of the disease to minimize perioperative complications.
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