Anaesthetic management for descompressive craniectomy in Chiari type I malformation in a patient with suspicion of mast cell activation syndrome

Authors

  • Fátima Ortiz Parra FEA Servicio de Anestesiología, Reanimación y Terapia del Dolor Complejo Hospitalario de Toledo.
  • M González De La Aleja FEA Servicio de Anestesiología, Reanimación y Terapia del Dolor, Hospital Universitario 12 de Octubre, Madrid.
  • Claudia Olea Vielba FEA Servicio de Anestesiología, Reanimación y Terapia del Dolor, Hospital Universitario 12 de Octubre, Madrid.

DOI:

https://doi.org/10.30445/rear.v12i1.803

Keywords:

Craniectomy, Mastocytosis, Anaesthesia, Chiari

Abstract

Mastocytosis is a rare disease whose management must be performed by any anaesthetist because of the clinical consequences that an innapropiate perioperative management may bring.  

Its clinical manifestations are due to the release of histamine and other pro-inflammatory substances holded by mast cells, triggered by multiple elements and many drugs: more specifically, many of the drugs we use in the anaesthetic procedure.

We present the case of a patient with suspicion of mast cell activation syndrome and many certified allergies, who was proposed to be operated on because of a Chiari type 1 malformation with syringomyelia.

References

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Published

2020-09-10

How to Cite

Ortiz Parra, F., González De La Aleja, M., & Olea Vielba, C. (2020). Anaesthetic management for descompressive craniectomy in Chiari type I malformation in a patient with suspicion of mast cell activation syndrome. Revista Electrónica AnestesiaR, 12(1), 2. https://doi.org/10.30445/rear.v12i1.803

Issue

Vol. 12 No. 1 (2020): Revista Electrónica de AnestesiaR

Section

Clinical case reports

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Copyright (c) 2020 Revista Electrónica AnestesiaR

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