Anesthetic challenges in a patient with gray platelet syndrome for cardiac surgery

Authors

  • Sara Cocho Crespo Specialist in anesthesiology, resuscitation and pain therapy. University Clinical Hospital of Valladolid.
  • Carla Del Rey De Cabo Specialist in anesthesiology, resuscitation and pain therapy. Zamora Healthcare Complex
  • Iciar Martínez-Almeida Castañeda Specialist in anesthesiology, resuscitation and pain therapy. University Clinical Hospital of Valladolid.

DOI:

https://doi.org/10.30445/rear.v15i10.1106

Keywords:

Gray platelet síndrome, cardiac surgery, anesthesia

Abstract

Gray platelet síndrome (GPS) is an uncommon platelet fuction disorder (<1:1000000) characterized by macrothrombocitopenia and hemorrhages. There are not established guidelines regarding perioperative management in patients with GPS, so the management is based on a few cases reported. The recommendations published on literature to prevent perioperative bleeding in the described patient are the use of tranexamic acid, desmopressin and platelet blood transfusión before each potencial bleeding procedure. In these article we describe the management of a patient with GPS who need cardiac surgery to repair mitral valve prolapse.

References

- Carrascal T, Laguna G, Blanco M, Segura B, Martínez-Almeida I. Gray platelet síndrome: Management of perioperative bleeding in redo cardiac surgety. J Card Surg. 2019;1-3

- Orsini S, Noris P, Bury L, et al. European Hematology Association- Scientific Working Grpup (EGA. SWG) on thrombocytopenias and platelet disorders. Bleeding risk of surgery and its prevention in patients with inherited platelet disorders. Haematologica. 2017; 102: 1192-1203

- Coppola A, Di Minno G. Desmopressin in inherited disorders of platelet function. Haemophilia 2008; 14(suppl 1): 31-39

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Published

2023-11-07 — Updated on 2023-11-08

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How to Cite

Cocho Crespo, S., Del Rey De Cabo, C., & Martínez-Almeida Castañeda, I. (2023). Anesthetic challenges in a patient with gray platelet syndrome for cardiac surgery. Revista Electrónica AnestesiaR, 15(10). https://doi.org/10.30445/rear.v15i10.1106 (Original work published November 7, 2023)

Issue

Vol. 15 No. 10 (2023): Revista Electrónica de AnestesiaR

Section

Clinical case reports

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Copyright (c) 2023 Revista Electrónica AnestesiaR

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