Enfermedad de Behçet en paciente joven. A propósito de un caso.

Ana Belén Rubio López; Sandra Pandiella Martinez; Cristina García Pérez; Eva María Higuera Miguélez

doi:10.30445/rear.v16i7.1224

Authors

Ana Belén Rubio López PhD. Anaesthesiology, Reanimation and Pain Therapeutics. Leon University Healthcare Complex.
Sandra Pandiella Martinez PhD. Anaesthesiology, Reanimation and Pain Therapeutics. Leon University Healthcare Complex.
Cristina García Pérez PhD. Anaesthesiology, Reanimation and Pain Therapeutics. Leon University Healthcare Complex.
Eva María Higuera Miguélez PhD. Anaesthesiology, Reanimation and Pain Therapeutics. Leon University Healthcare Complex.

DOI:

https://doi.org/10.30445/rear.v16i7.1224

Keywords:

Behcet's disease, Gastrointestinal involvement in Behçet., anesthetic implications

Abstract

Behçet's disease is a systemic vasculitis characterised by recurrent oral and genital aphthae associated with ocular, vascular and cutaneous disease. Clinical manifestations including arthritis, gastrointestinal involvement and central and peripheral nervous system disease. These lesions are the result of inflammation or vasculitis of blood vessels of all sizes on both the arterial and venous sides of the circulation (1,2,3).

We present the clinical case of a young black woman with long-standing Behçet's disease complicated by severe neurological involvement, on chronic treatment with high doses of corticosteroids, who needed emergency surgery for spontaneous intestinal perforations on two times.

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